Supratentorial hemangioblastoma without von Hippel-Lindau syndrome in an adult A rare case report

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Oguz Baran
Omur Kasimcan
Aydin Sav
Hakan Oruckaptan4

Abstract

Hemangioblastomas (HBLs) are highly vascular and cystic benign neoplasms. They form very small part of intracranial tumours and are often localized in the posterior fossa. Although most of them are sporadic, a significant group is accompanied with von Hippel-Lindau (VHL) syndrome.


This case report presents a 57-year-old woman treated with total resection using micro-surgical technique and was diagnosed as HBL based on histopathologic findings. Contrast-enhanced cranial MRI of the patient with the complaints of spasms in the right side of body showed a right paracentral mass that caused midline shift.


In literature, the previously reported cases of supratentorial HBL unaccompanied with VHL syndrome were searched in PUBMED, compiled and presented. It should be borne in mind that rare HBLs manifesting with various neurological symptoms may occur in the supratentorial region, and may not accompany with VHL syndrome.

Article Details

How to Cite
Baran, O., Kasimcan, O., Sav, A., & Oruckaptan4H. (2019). Supratentorial hemangioblastoma without von Hippel-Lindau syndrome in an adult. Romanian Neurosurgery, 33(3), 337-344. https://doi.org/10.33962/roneuro-2019-058
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Articles
Author Biographies

Oguz Baran

Haseki Research and Training Hospital, Neurosurgery Clinic, Istanbul, TURKEY

Omur Kasimcan

Istinye University, Neurosurgery Clinic, Istanbul, TURKEY

Aydin Sav

Department of Pathology, School of Medicine, Yeditepe University, Istanbul, TURKEY

Hakan Oruckaptan4

Memorial Hospital, Neurosurgery Clinic, Ankara, Turkey

*Our senior author was deceased in the writing process of the article