Sturge Weber Syndrome Review of literature with case illustration

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Guru Dutta Satyarthee
Manik Prabhu
Luis Rafael Moscote-Salazar

Abstract

Sturge-Weber syndrome (SWS) also called as encephalotrigeminal angiomatosis, is a sporadically occurring rare neuro-cutaneous syndrome, characterized by vascular malformation with capillary venous angiomas involving face, choroidal layer of eye globe and leptomeninges responsible for ophthamological as well as neurological signs and symptoms. Authors report an interesting case, a six year old girl, who presented with seizures, facial port wine stain and normal psychomotor development. CT scan showed left cerebral hemiatrophy, left frontal and parieto occipital calcification with cortical calcification in left high frontal convexity. Cranial MRI scan also confirmed finding of left cerebral hemiatrophy and also revealed presence of gyriform cortical calcification, prominent flow voids seen in left basal ganglia. Her seizure is well controlled with antiepileptic medication. The pertinent literature is reviewed and management of such cases is discussed briefly.

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How to Cite
Satyarthee, G. D., Prabhu, M., & Moscote-Salazar, L. R. (2017). Sturge Weber Syndrome: Review of literature with case illustration. Romanian Neurosurgery, 31(1), 122–128. Retrieved from https://www.journals.lapub.co.uk/index.php/roneurosurgery/article/view/981
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Articles
Author Biographies

Guru Dutta Satyarthee

Department of Neurosurgery, AIIMS New Delhi, INDIA

Manik Prabhu

Department of Neurosurgery, AIIMS New Delhi, INDIA

Luis Rafael Moscote-Salazar

Neurosurgeon-Critical Care, RED LATINO. Latin American Trauma & Intensive Neuro-Care Organization, Bogota, COLOMBIA